Orphanet: Syndrome congenital d hamartome hypothalamique. Request PDF on ResearchGate | On Jul 1, , J. Mounach and others published Puberté précoce liée à un hamartome hypothalamique. Request PDF on ResearchGate | On May 1, , N. Ech-Cherif El Kettani and others published Hamartome hypothalamique révélant des crises gélastiques.

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You can move this window by clicking on the headline. Classification and possible treatment selection for hypothalamic hamartoma HH modification from Choi et al. Furthermore, they did not suggest any treatment strategy for Type 2 sessile HHs.

Cognitive functioning before and after surgical resection for hypothalamic hamartoma and epilepsy. CT, MR, and pathologic findings. Abstract Hypothalamic hamartoma HH is a benign indolent lesion despite the presentation of refractory epilepsy. Open in a separate window. However, disconnection from the brain for controlling intractable epilepsy would be always feasible regardless of HH size.

hypothalamus hamartome – Translation into English – examples French | Reverso Context

Electrophysiological properties of human hypothalamic hamartomas. Journal page Archives Contents list. Top of the page – Article Outline.

Thus, the authors performed an endoscopic disconnection only for the intraventricular type of hamartoma Type III. High frequency stimulation of the mamillothalamic tract for the treatment of resistant seizures associated with hypothalamic hamartoma.


This rare non-neoplastic abnormal mixture of neuronal and glial tissue of the inferior hypothalamus has been postulated to be derived from the mammillo-thalamo-cingulate tract from which Hypothalajique is networking other brain areas associated with GS or the pathway from the HH to the brainstem and cerebellum 16 As the authors describe 31even giant HHs larger than 25 mm can be efficiently disconnected under guidance of a depth electrode and frameless neuronavigation system.

Utility of early single photon emission computed tomography SPECT in neonatal gelastic epilepsy associated with hypothalamic hamartoma. Endoscopic hypothwlamique to hypothalamic hamartoma HHs.

Bourazza aH. Neurol Med Chir Tokyo ; The histopathology of hypothalamic hamartomas: In bilateral attachment and giant HH cases, preoperative electrophysiological evaluation mostly revealed unilateral propagation of epileptiform discharge 31 Surgical approaches to hypothalamic hamartomas.

The direction will be posterior to anterior and lateral to inferior midline Fig.

Orphanet: Syndrome congenital d hamartome hypothalamique

Ictogenesis and symptomatogenesis of gelastic seizures in hypothalamic hamartomas: Villeneuve abHamartme. There should be minimal working space within the third ventricle for forceps and coagulator, as well as definite interface either on the neuronavigational image or direct visualization.

Outline Masquer le plan. As per the Law relating to information storage and personal integrity, you have the right to oppose art 26 of that lawaccess art 34 of that law and rectify art 36 of that law your personal data.


Endoscopic Treatment of Hypothalamic Hamartomas

Delalande O, Fohlen M. Contact Help Who are we? Endoscopic surgery for hypothalamic hamartomas causing medically refractory gelastic epilepsy.

Stereotactic Laser Ablation for Hypothalamic Hamartoma. Relatively small ventricle and foramen of Monro. Contact Help Who are we?

Deep brain stimulation for the treatment of drug-refractory epilepsy in a patient with a hwmartome hamartoma. But even though HHs attach to the bilateral hypothalamus, unilateral hypothaamique is usually enough. It has been well known that epileptic discharge originates from the hamartoma itself and propagates to subcortical and cortical areas. The owners of this website hereby guarantee to respect the legal confidentiality conditions, applicable in France, and not to disclose this data to third parties.

Other types of seizure, cognitive deterioration, and behavioral uamartome follow and frequently develop late in the first decade of life 4 Zerhouni aA. Disconnecting surgical treatment of hypothalamic hamartoma in children and adults with refractory epilepsy and proposal of a new classification.

Epileptic network of hypothalamic hamartoma: From hypothalamic hamartoma to cortex: Endocrine assessment would include sex hormone and growth hormone levels, thyroid function, prolactin level, and cortisol reserve with glucagon stimulation.